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An overview of Wolman Disease

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Wolman disease is generally described as a rare form which is also called an inherited health condition which usually involves the breakdown of cholesterol and fats in every individual’s body or else 'lipid metabolism’. People who are affected by this Wolman disease disorder will face the harmful amounts of lipids which are collecting in their liver, spleen, small intestine, bone marrow, lymph nodes, and adrenal glands. And affected people will also experience calcium deposits in their adrenal glands. When an infant is born with Wolman disease, they are active and healthy. Children who are affected with Wolman disease will develop severe malnutrition. Most children do not live beyond their childhood. This type of disorder will occur approximately in one in 350k newborns. Other names of Wolman disease are Acid Lipase Deficiency, Familial Xanthomatosis, Lipa Deficiency, LAL deficiency, Liposomal Acid Lipase Deficiency, and Lysosomal Acid Lipase Deficiency. Wolman disease typically co...